Stoma takedown after Hartmann’s procedure in a patient with hemophilia A complicated with production of inhibitor to FVIII (review and case report)
https://doi.org/10.33878/2073-7556-2022-21-4-130-138
Abstract
One of the specific manifestations of hemophilia A is the spontaneous abdominal hematoma mimicking the clinical picture of acute abdominal disease. The appearance of auto-antibodies to FVIII leads to a loss of response to replacement hemostatic therapy and requires an individualized approach as well as highly sensitive laboratory monitoring to reduce the risk of uncontrolled bleeding. The paper presents the case of multi-stage surgical treatment of this complication.
About the Authors
S. V. Shtyrkova
National Medical Research Center for Hematology
Russian Federation
Russian Federation
Shtyrkova Svetlana V.
Novy Zykovsky proezd, 4, Moscow, 125167
mobile: +7 (916) 136-04-21, office: +7 (495) 612-61-91
S. A. Shutov
National Medical Research Center for Hematology
Russian Federation
Russian Federation
Novy Zykovsky proezd, 4, Moscow, 125167
P. A. Batrov
National Medical Research Center for Hematology
Russian Federation
Russian Federation
Novy Zykovsky proezd, 4, Moscow, 125167
E. G. Rybakov
National Medical Research Center of Coloproctology
Russian Federation
Russian Federation
Salyama Adilya str., 2, Moscow, 123423
N. V. Prasolov
National Medical Research Center for Hematology
Russian Federation
Russian Federation
Novy Zykovsky proezd, 4, Moscow, 125167
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Review
For citations:
Shtyrkova S.V., Shutov S.A., Batrov P.A., Rybakov E.G., Prasolov N.V. Stoma takedown after Hartmann’s procedure in a patient with hemophilia A complicated with production of inhibitor to FVIII (review and case report). Koloproktologia. 2022;21(4):130-138. https://doi.org/10.33878/2073-7556-2022-21-4-130-138
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